Type 1 autoimmune pancreatitis: a diagnostic challenge with an atypical presentation

Abstract

Autoimmune pancreatitis (AIP) is a rare chronic inflammatory disease of the pancreas with benign behavior, typical histologic findings and a positive response to corticosteroid treatment. Although there are well standardized criteria to establish its diagnosis, sometimes its presentation may raise doubts with other diseases affecting the pancreas, such as adenocarcinoma and pancreatic cystic neoplasms. We present the case of a 51-year-old male debuting with constitutional symptoms and radiological findings which suppose a challenge in differential diagnosis of pancreatic pathology.

Keywords: autoimmune pancreatitis, pancreatic collection, differential diagnosis.